WOFAPS 2025 8th World Congress of Pediatric Surgery

Rong Zhang, TengHui Zhan

Fujian Maternity and Child Health Hospital

Background: The Budd-Chiari Syndrome (BCS) is characterized by the hepatic venous outflow obstruction, which is rare in infants or children. Endovascular treatment is possible for managing chronic BCS in children with 2-16 years of age, but no previous reports of successful endovascular therapy in neonates exist.

Case presentation: A 5-day-old male neonate was admitted to the neonatal intensive care unit due to inferior vena cava hepatic segment atresia on prenatal color Doppler ultrasound (CDUS), poor appetite after birth, and postnatal CDUS showing inferior vena cava hepatic segment strong echo. He was diagnosed with Budd-Chiari syndrome and underwent endovascular treatment. On the fourth day after the operation, his liver function indicators returned to normal, and he was healthy at the 1-year follow-up.

Conclusion: The early aggressive endovascular therapy might be feasible in treating neonatal BCS. The short-term efficacy were acceptable, and the long-term efficacy required further follow-up.