WOFAPS 2025 8th World Congress of Pediatric Surgery

Cheena Kumari, Syed Waqas Ali, Muhammad Arif Mateen Khan, Aiman Khan

Department of Pediatric Surgery, Dow University of Health Sciences / Dr Ruth KM Pfau Civil Hospital, Karachi, Sindh, Pakistan

Introduction: Ectopic pancreas and gastrointestinal (GI) duplication are rare congenital anomalies. The occurrence of acute pancreatitis due to ectopic pancreatic tissue within a GI duplication is extremely uncommon.

Case presentation: We report the case of an 8-year-old boy with a history of recurrent pancreatitis who was referred for further evaluation. An upper GI series suggested intestinal malrotation. Ultrasound revealed a thickened mesentery with free fluid in the pelvis. During surgical exploration, multiple small bowel adhesions were found, and the duodenojejunal flexure (DJF) was abnormally located to the right of the spine. A 2.5 cm × 2.5 cm ectopic glandular tissue was noted on the jejunal wall, along with a 9 cm × 5 cm tubular duplication distal to the DJF, followed by resection and anastomosis. Histopathological examination confirmed benign pancreatic tissue in the ectopic site and nonspecific inflammatory changes in the duplicated jejunal segment. The patient had an uneventful postoperative recovery.

Conclusion: This case illustrates the rare combination of jejunal duplication cyst, malrotation, and ectopic pancreatic tissue in a pediatric patient. Surgical management is crucial for both therapeutic and diagnostic purposes.