WOFAPS 2025 8th World Congress of Pediatric Surgery

İbrahim Yıldırım, Özcan UZUN, Sevim Ecem Ünlü Ballı, Fatma Bilgecan Şimşek, Mehmet Bahadır Çalışkan, Gökhan Berktuğ Bahadır, İlhami Sürer, Suzi Demirbağ

Department of Pediatric Surgery, Health Sciences University Gulhane Medical Faculty

Congenital pulmonary airway malformation (CPAM) is the most common type of congenital lung malformation, accounting for approximately 25% of all congenital lung anomalies. We aimed to present the operative video of an 8-year-old girl who underwent thoracoscopic right lower lobectomy with a prediagnosis of CPAM.

An 8-year-old girl who had many problems due to respiratory tract infections but did not present to the hospital was admitted to an external center with a cough and fever for about 2 weeks. Computed tomography (CT) revealed multiple cysts and abscesses in the right lower lobe and the patient was referred to our center. Pneumonia was detected at the time of admission. After treatment of the infection, a control CT scan was performed and showed an appearance compatible with type 2 CPAM. Thoracoscopic right lower lobectomy was performed. The thoracic tube was withdrawn on postoperative day 5. He was discharged on the 6th postoperative day with no problem. In the follow-up chest radiography, the right lung was expanded.

In conclusion, CPHYM is a rare pathology. In children who present with respiratory distress and do not respond to treatment, CPCPC should be considered after excluding common clinical conditions.