WOFAPS 2025 8th World Congress of Pediatric Surgery

Mohamed Helali, Isam Taha

National Ribat University Hospital

Introduction:

Intrathoracic ectopic kidney (ITEK) is a rare congenital anomaly occurring in <5% of renal ectopias, often asymptomatic and detected incidentally. Pulmonary sequestration, another rare malformation, involves non-functioning lung tissue with systemic blood supply. We report the first documented case in Sudan of concurrent ITEK and pulmonary sequestration without diaphragmatic hernia.

Case Presentation:

A 7-month-old male with recurrent respiratory distress since birth presented with failure to thrive and breastfeeding difficulties. Imaging revealed a right thoracic kidney and adjacent lung mass. Thoracotomy confirmed an ectopic kidney adherent to a sequestrated lung lobe. The sequestration vessels were ligated, and the lung was successfully decorticated while preserving the thoracic kidney. Postoperative recovery was uneventful with resolution of symptoms.

Conclusion:

This unprecedented combination highlights diagnostic challenges in pediatric respiratory cases. CT imaging was critical for preoperative planning. Conservative management of the asymptomatic ITEK with surgical correction of sequestration yielded excellent outcomes. The case underscores the need for high clinical suspicion of rare congenital anomalies in refractory pediatric respiratory presentations.

Conflict of Interest:

The authors declare no conflict of interest.